Ormond’s Disease – a case report
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Klinika Chorób Wewnętrznych i Reumatologii CSK MON WIM w Warszawie; kierownik: prof. dr hab. n. med. Witold Tłustochowicz
Zakład Radiologii Lekarskiej CSK MON WIM; kierownik: dr n. med. Artur Maliborski
Submission date: 2018-04-03
Publication date: 2018-06-25
LW 2018;96(3):241-244
Retroperitoneal fibrosis, also called Ormond’s Disease, is a chronic inflammatory process, characterized by the development of combined fibroid and inflammatory tissue in the retroperitoneal space. Typically, lesions are located in the retroperitoneal space of abdominal arteries, iliac arteries, ureters, and sometimes duodenum or kidneys. In the majority of cases the disease is primary (idiopathic retroperitoneal fibrosis – IRPF), rarely is secondary to drugs, malignancy, radiotherapy or infections. RPF is an uncommon condition, mostly affecting people in their 50s, and prevalent to the males. Diagnosis can be made on the basis of clinical manifestation and results of the medical imaging. If the clinical presentation is unusual or the location of fibrosis is untypical, the biopsy of the fibroid should be made to confirm the recognition. Currently, there is no recommendation of treatment of the RPF, mostly a therapy scheme is based on the experience of specialized centers and rare publications. The article presents the case of 62‑year‑old female hospitalized in the Department of Internal Diseases and Rheumatology due to inflammation of the peripheral joints, who was diagnosed as RPF during conventional diagnostics. The patient was successfully treated with an immunosuppressive therapy.
No conflicts of interest were declared.
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